Emergency Help

FOP is a genetic disorder in which bone forms in muscles, tendons, ligaments and other connective tissues.

When treating a patient with FOP, MINIMISE RISK with EXTRA CARE IN ALL SITUATIONS

To minimise the risk of FOP flares and subsequent extra bone growth (which can be unpredictable or caused by trauma), take extra care in all situations.

Avoid triggers such as deep invasive procedures, repeated or excessive blood pressure cuff inflation, and forced joint movement or stress.

Ensure medical care minimises trauma by, for example, using experienced staff for blood draws and reducing the frequency of blood pressure measurements to the minimum required.

However, in all cases: protect the life of the patient as though FOP was not an issue

In all cases: protect the life of the patient as though FOP was not an issue

Where possible, follow these guidelines, along with the treatment guidelines.  Any unnecessary physical trauma to the patient can cause irreparable restrictions to their body and movements.

1. Avoid deep tissue trauma

Including intramuscular (IM) injections, if possible.

2. Stabilize & treat

NO IM injections but venepuncture, subcutaneous and intravenous medications are okay.

3. Take intubation precautions

Protect the jaw and get expert anaesthesia assistance since the jaw and neck may be completely or partially locked.  If airway management is needed, the preferred approach is naso-trachael intubation with fibre-optic guidance.  Many people with FOP have restricted jaw and neck mobility, so intubation must be done in as gentle a fashion as possible.  Follow intubation with a course of steroids (prednisolone 2mg/kg/day for 4 days) to prevent fatal airway swelling from the trauma.

4. Consult expert doctors

This is strongly recommended regarding the potential risks of any surgical or medical interventions being considered.

5. Consider administering prophylactic (precautionary) steroids in cases of major trauma

Emergency Medical Contacts